a.k.a. Lissencephaly Syndrome
Airway:
Microcephaly
Micrognathia
Cleft palate
Respiratory:
Recurrent aspiration pneumonia
Cardiovascular:
ASD
VSD
TOF
PS
Gastrointestinal:
GERD
Dysphagia
Omphalocele
Genitourinary
Cryptorchidism
Neurological:
Lissencephaly
Developmental delay
Seizures
Hypotonia
Musculoskeletal:
Clinodactyly
Polydactyly
Considerations:
Challenging induction 2° mental delay
Difficult laryngoscopy 2° micrognathia
Aspiration risk
Post-operative respiratory complications
Altered drug metabolism 2° to seizure medications
Consider SBE prophylaxis
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