Megalencephaly
Airway:
Copious oral secretions
Large head
Gastrointestinal:
GERD
Neurological:
Seizures
Progressive spasticity & dementia
Hydrocephalus
Considerations:
Aspiration risk
Positioning challenges
Anticonvulsants may affect drug metabolism
Avoid phenothiazines, butyrophenones, metoclopramide, dopaminergic blockers which may affect movement disorders
Links:
Adrenoleukodystrophy
Metachromatic Leukodystrophy
Krabbe disease
Canavan disease
Pelizaeus-Merzbacher disease
References:
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