Alagille Syndrome

Arteriohepatic dysplasia

Airway:
Pointed mandible

Cardiovascular:
Pulmonary stenosis
Peripheral pulmonary stenosis
Occ. TOF, ASD, VSD, Coarctation

Gastrointestinal:
Intrahepatic biliary atresia, hypoplasia
Cirrhosis
Esophageal varices

Endocrine:
Hypercholesterolemia
Hyperlipidemia

Neurological:
Intracranial hemorrhage
Hepatic encephalopathy
Carotid/intracranial aneurysms

Musculoskeletal:
Growth retardation

Considerations:
Cardiac, hepatic, renal status
SBE prophylaxis
Bleeding issues